Sociedad de Pediatría de Andalucía Occidental y Extremadura

Septo-optic dysplasia or Morsier syndrome, which consists in the association of hypoplasia of the optic nerves, the agenesis of septum pellucidum, and deficiency of secretion of hypothalamicpituitary hormones. We present a clinical case of septo-optic dysplasia followed in our center. Patient who is currently 4 years old. She was diagnosed in the first months of life. At follow-up it is confirmed that it associates a deficit of growth hormone. Growth hormone treatment is approved with auxologic criteria, the patient shows an excellent response to substitution treatment with growth hormone.